SCLEROZA TUBEROASA

0
8

SCLEROZA TUBEROASA (BOURNEVILLE) / scl6rose tub6- reuse (de Bourneville) / tuberous sclerosis. [Desire Maglo- irc ISouriicvi llc, muro[og fiuricez, ‘Paris, 1840-1909. *Faco- matoza cu leziuni cutanate (adenoame sebacee ale fetei si *tumori Koenen periungveale, care reprezinta un semn pato- gnomonic) $i cerebrale, constand in calcificari multiple. Simpto- matologia consta in tulburari nervoase (paralizii, convulsii) si psihice (deficit intelectual, tulburari de comportament). Sin.: boala Bourneville, epiloia.