SINDROM PAPILLON LEAGE

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SINDROM PAPILLON LEAGE-PSAUME / s. Papi llon L6age-Psaume / familial orofaciodigital dysostosis. [Elmr Papiffon Ledge, stomatoCog fraiice-z, contemporan; Jean Psaume, stomatoCog frawez, n, 1920.} Sin.: sindromorodigitofacial de tip I (v.). ‘ S. PAPILLON-LEFEVRE. [M. M. Papillon, dennatohg frances contemporan; Paul Lefovi-v, de.rmato[og francez; ‘Paris, n. 1891.} Q. ereditar, transmis autozomal recesiv, caracterizat prin hiperkeratoza palmo-plantara si anomalii dentare. V. keratoder- mie si boala Meleda.