KERATOZA DISEMINATA CIRCUMSCRISA

0
9

KERATOZA DISEMINATA CIRCUMSCRISA / k6ratose disse- minee circonscrite / dyskeratosis congenita. Distrofie con- genitala si familiala (cu transmitere dominants) caracterizata prin papule oomoase foliculare confluente, asodate cu keratoder-mie palmoplantara, pahionichie, leucokeratoza bucala, kerati-nizari corneene si tulburari psihice. Sin.: boala J adassohn- Lewandowsky, pahionichie congenitala.