BOALA KUFS. [Hugo Kufs, neuroCog, Leipzig, 1871-1955.} Forma tardiva de ‘idiotie amaurotica familiala, caracterizata prin apa- ritia, la adult, a unei deficiente mentale progresive, msotita de semne cerebeloase si extrapiramidale, cu evolutie lent progre- siva, dar prognostic letal. Sin.: sfingolipidoza de tip adult.