SINDROM CRIGLER

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SINDROM CRIGLER-NAJJAR. |/o/in Fielding Criglor, pediatni. ame- ril.’a.n, n, 1919; Victor A. Nuj ji ir, pediatni american, n. 1914.} Deficit congenital de glucuronil transferaza (enzima care inter- vine in *glicuronoconjugare), transmis autozomal recesiv. Se manifesta sub doua forme: complet (I), forma grava, mergand pana la encefalopatie hiperbilirubinemica, si parJial (II), fara anomalii neurologice. Sin.: icter familial congenital Crigler-Najjar.